Objective To report 1 case of a child ureteral inflammatory myofibroblastoma (IMT), combined with the literature, review its clinicopathological features, diagnosis and differential diagnosis. Methods The case was conventional HE and adjuvant immunohistocchemical staining. Results The tumor tissue is composed of spindle cells and is arranged in a fascicular or woven arrangement, immunohistochemical staining showed that the tumor cells were positive for SMA、vimentin ，pathological diagnosis: Inflammatory myofibroblastoma. Conclusion IMT is a rare soft tissue tumor, diagnosis was mainly based on pathological diagnosis and immunohistochemistry staining, differential diagnosis has rhabdomyosarcoma,Differential diagnosis has rhabdomyosarcoma, fibromatosis, low malignancy fibrosarcoma, nodular fasciitis, leiomyosarcoma.